Case of cardiac fibroma of the right ventricle of the heart in a girl of 1 year 3 months age is described. Clinically, the tumor had an asymptomatic course, which was interrupted by sudden occurrence of heart failure with attacks of the paroxysmal ventricular tachycardia. Fibroma had a typical histological structure at the pathomorphology. The death of a child occurred during the surgical treatment initiated due to vital indications, being a result of cardiac failure due to cardiogenic shock. Tumors of the heart are a rare pathology in childhood, difficult for timely diagnosis and treatment.